PDF(Pubmed)
Abstract：
We present a case of a 76-year-old Caucasian female with a recurrent solitary fibrous tumor (SFT) of the pleura, showcasing a rare manifestation of hypoglycemia associated with Doege-Potter syndrome (DPS). Having undergone two previous surgeries for SFT, the patient presented to the emergency department with severe fatigue, recurrent episodes of loss of consciousness, and hypoglycemia, despite lacking a history of diabetes mellitus. Radiological evaluation revealed a substantial recurrent SFT in the left lung, prompting excision through a left posterolateral thoracotomy. Remarkably, the patient\'s altered mental status and hypoglycemia resolved postoperatively. The case meets the criteria for aggressive SFT behavior, warranting consideration for adjuvant radiation therapy to control the risk of recurrence. This report highlights the nuanced interplay between SFT recurrence, paraneoplastic syndromes like DPS, and the potential benefits of adjuvant therapeutic strategies in managing these complex clinical scenarios.
摘要：
我们介绍了一例76岁的高加索女性，其胸膜复发性孤立性纤维瘤（SFT），显示与Doege-Potter综合征（DPS）相关的低血糖的罕见表现。之前接受过两次SFT手术，患者出现严重疲劳到急诊科，反复发作的意识丧失,和低血糖，尽管没有糖尿病病史。放射学评估显示左肺有大量复发性SFT，提示通过左后外侧开胸手术切除。值得注意的是,患者的精神状态改变和低血糖在术后缓解。该案例符合激进SFT行为的标准，保证考虑辅助放射治疗以控制复发风险。本报告强调了SFT复发、副肿瘤综合征如DPS,以及辅助治疗策略在管理这些复杂临床情景方面的潜在益处。
