PDF(Pubmed)
Abstract：
BACKGROUND: Mounier-Kuhn syndrome (MKS) is a rare disorder characterized by abnormal dilation of the trachea and main bronchi. MKS can be easily missed on chest X-rays, making diagnosis difficult. Under general anesthesia, challenges such as airway leakage or collapse during mechanical ventilation may complicate the achievement of adequate tidal volumes.
METHODS: A 94-year-old woman requiring emergency hemiarthroplasty of the hip under general anesthesia was admitted. Preoperative chest X-rays revealed dilation of the trachea and main bronchi, but the patient exhibited no respiratory symptoms. We diagnosed her with MKS and opted for an 8.0-mm-inner-diameter reinforced tracheal tube. We positioned the cuff in the subglottic area, inflating it while monitoring for air leakage. Throughout the surgery, adequate tidal volume was maintained.
CONCLUSIONS: Anesthesiologists must conduct a comprehensive evaluation of patients with MKS, including a review of chest radiographs, and establish a meticulous anesthesia plan prior to surgery.
METHODS: A 94-year-old woman requiring emergency hemiarthroplasty of the hip under general anesthesia was admitted. Preoperative chest X-rays revealed dilation of the trachea and main bronchi, but the patient exhibited no respiratory symptoms. We diagnosed her with MKS and opted for an 8.0-mm-inner-diameter reinforced tracheal tube. We positioned the cuff in the subglottic area, inflating it while monitoring for air leakage. Throughout the surgery, adequate tidal volume was maintained.
CONCLUSIONS: Anesthesiologists must conduct a comprehensive evaluation of patients with MKS, including a review of chest radiographs, and establish a meticulous anesthesia plan prior to surgery.
摘要：
背景：Mounier-Kuhn综合征（MKS）是一种罕见的疾病，其特征是气管和主支气管异常扩张。MKS在胸部X光片上很容易漏掉,使诊断变得困难。在全身麻醉下,机械通气期间的气道渗漏或塌陷等挑战可能会使实现足够的潮气量复杂化。
方法：收治一名94岁女性，需要在全身麻醉下进行紧急人工髋关节置换术。术前胸部X光显示气管和主支气管扩张，但患者没有出现呼吸道症状。我们诊断她患有MKS，并选择了8.0毫米内径的增强型气管导管。我们把袖带放在声门下区,充气，同时监测空气泄漏。在整个手术中,保持了足够的潮气量。
结论：麻醉医师必须对MKS患者进行全面评估，包括胸部X光片的检查,并在手术前制定细致的麻醉计划。
方法：收治一名94岁女性，需要在全身麻醉下进行紧急人工髋关节置换术。术前胸部X光显示气管和主支气管扩张，但患者没有出现呼吸道症状。我们诊断她患有MKS，并选择了8.0毫米内径的增强型气管导管。我们把袖带放在声门下区,充气，同时监测空气泄漏。在整个手术中,保持了足够的潮气量。
结论：麻醉医师必须对MKS患者进行全面评估，包括胸部X光片的检查,并在手术前制定细致的麻醉计划。
