关键词: Systemic lupus erythematosus cutaneous lupus vasculitis

Mesh : Humans Female Adult Complement C1q / deficiency Lupus Erythematosus, Systemic / complications diagnosis Vasculitis / diagnosis drug therapy Urticaria / diagnosis Rituximab / therapeutic use Lupus Nephritis / diagnosis complications drug therapy Diagnosis, Differential

来  源:   DOI:10.1177/09612033241253156

Abstract:
In rare instances, patients with SLE may exhibit atypical clinical manifestations, such as Hypocomplementemic Urticarial Vasculitis, which can pose diagnostic challenges. Here, we present a case report of a 28-year-old female with a history of SLE with lupus nephritis clase IV who developed HUV-like symptoms, ultimately leading to a diagnosis of C1q Vasculitis. This case underscores the importance of considering C1q Vasculitis in SLE patients presenting with HUV-like features and highlights Rituximab as a promising therapeutic option for managing this rare condition.
摘要:
在极少数情况下,SLE患者可能表现出不典型的临床表现,如低补体血症性荨麻疹性血管炎,这可能会带来诊断挑战。这里,我们提供了一例28岁女性,有SLE伴狼疮性肾炎IV病史,出现HUV样症状,最终导致C1q血管炎的诊断。该病例强调了在具有HUV样特征的SLE患者中考虑C1q血管炎的重要性,并强调了利妥昔单抗是治疗这种罕见疾病的有希望的治疗选择。
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