关键词: Lung agenesis PFT Pulmonary hypertension TB infection congenital malformation hypoplasia

来  源:   DOI:10.12890/2024_004421   PDF(Pubmed)

Abstract:
Lung underdevelopment is a rare congenital anomaly with variable clinical significance and presenting symptoms. It usually manifests during childhood. We present two cases of developmental lung anomaly subtypes and discuss clinical presentation and outcomes in such patient populations.
CONCLUSIONS: Pulmonary underdevelopment is a challenging diagnosis and should be considered in patients with unilateral opacification on chest radiograph.Childhood developmental history is critical for diagnosis as delayed, or misdiagnoses are common. Definitive diagnosis can be made by computed tomography scan.Management is watchful waiting with close monitoring, with long term prognosis remaining unclear.
摘要:
肺发育不良是一种罕见的先天性异常,具有不同的临床意义并表现出症状。它通常表现在童年。我们介绍了两例发育性肺异常亚型,并讨论了此类患者人群的临床表现和结果。
结论:肺发育不全是一个具有挑战性的诊断,在胸部X线片上单侧混浊的患者应考虑。童年发育史对于延迟诊断至关重要,或误诊是常见的。可以通过计算机断层扫描进行明确的诊断。管理层在密切监测的情况下保持警惕,长期预后仍不清楚。
公众号