关键词: felty syndrome multiple autoimmune syndrome neutropenia rheumatoid arthritis sle splenomegaly

来  源:   DOI:10.7759/cureus.57468   PDF(Pubmed)

Abstract:
Autoimmune diseases can result in additional symptoms and complications impacting various organ systems beyond the joints. These can affect the eyes, skin, respiratory, cardiac, and renal systems. Recognizing and understanding these diverse manifestations, such as the severe eye issues seen in rheumatoid arthritis (RA) and the potentially life-threatening Felty syndrome, is crucial for clinicians to promptly identify and treat these conditions effectively. In this case presentation, we report on a patient admitted for bilateral scleritis, which was found to be secondary to multiple autoimmune syndrome type 3. During the patient\'s hospital stay, Felty syndrome was incidentally diagnosed due to the observed combination of RA, splenomegaly, and absolute neutropenia. Prompt recognition of this condition allowed the patient to receive appropriate care, including oral steroids, hydroxychloroquine, and methotrexate, decreasing the risk of severe complications.
摘要:
自身免疫性疾病可导致影响关节以外的各种器官系统的额外症状和并发症。这些会影响眼睛,皮肤,呼吸,心脏,和肾脏系统。认识和理解这些不同的表现形式,例如在类风湿性关节炎(RA)中看到的严重眼部问题和可能危及生命的Felty综合征,对于临床医生及时识别和有效治疗这些疾病至关重要。在这种情况下,我们报道了一名因双侧巩膜炎入院的患者,被发现继发于3型多重自身免疫综合征。在病人住院期间,由于观察到的RA组合,偶然诊断出Felty综合征,脾肿大,和绝对中性粒细胞减少症。对这种情况的迅速认识使患者能够接受适当的护理,包括口服类固醇,羟氯喹,和甲氨蝶呤,降低严重并发症的风险。
公众号