Abstract:
Diabetic striatopathy (DS) is a rare and life-threatening mani- festation of diabetes. The disease commonly affects individuals of Asian descent, women and the elderly. DS is characterized by dyskinesias with basal ganglia hyperintensities on imaging. Despite being rare, prompt recognition of a hyperglycaemia- induced hemichorea-hemiballismus is essential because the symptoms are reversible with correction of hyperglycaemia. Diagnosis is based on blood analysis and neuroimaging findings. Laboratory tests reveal raised glycosylated haemoglobin (HbA1c) levels, which indicate poorly controlled diabetes. Neuroimaging provides suggestive findings of DS. It is usually associated with non-ketotic hyperglycaemia. We report a 50-year-old woman who presented with ketotic hyperglycaemia and left-sided hemichorea and partial seizures with secondary generalization.
摘要:
糖尿病性纹状体病(DS)是一种罕见且危及生命的糖尿病患者。这种疾病通常会影响亚洲血统的人,妇女和老人。DS的特征是运动障碍,影像学上有基底神经节高信号。尽管罕见,及时识别高血糖引起的半球性偏瘫是必不可少的,因为通过纠正高血糖,症状是可逆的。诊断基于血液分析和神经影像学检查结果。实验室检测显示糖化血红蛋白(HbA1c)水平升高,这表明糖尿病控制不佳。神经影像学提供了DS的暗示性发现。它通常与非酮症性高血糖症有关。我们报告了一名50岁的妇女,她患有酮症性高血糖症,左侧偏球症和部分癫痫发作,并伴有继发性泛化。