关键词: Evans tumor low‐grade fibromyxoid sarcoma retroperitoneal sarcoma

来  源:   DOI:10.1002/iju5.12718   PDF(Pubmed)

Abstract:
UNASSIGNED: Low-grade fibromyxoid sarcoma is an uncommon deep-seated soft-tissue sarcoma that occurs rarely in young adults and children. Although surgical resection provides a long-term prognosis, late local recurrence and metastasis may occur.
UNASSIGNED: A 44-year-old woman with no prior medical history presented with breathing and abdominal discomfort. Contrast-enhanced computed tomography scan revealed a retroperitoneal tumor protruding into the thoracic cavity and pleural effusion on the left side. Tumor biopsy revealed sarcoma. We performed complete resection of the tumor along with part of the diaphragm and replaced the diaphragm with a prosthetic patch. Histopathologic findings indicated low-grade fibromyxoid sarcoma. The patient experienced no postoperative complications and received no adjuvant therapy. Furthermore, she survived 4 years after surgery without recurrence.
UNASSIGNED: Complete surgical resection is effective for low-grade fibromyxoid sarcoma; therefore, it is important to plan appropriately for complete resection when biopsy reveals malignant findings.
摘要:
低度纤维粘液样肉瘤是一种罕见的深部软组织肉瘤,很少发生在年轻人和儿童中。尽管手术切除提供了长期预后,可发生晚期局部复发和转移。
一名44岁女性,无既往病史,出现呼吸和腹部不适。对比增强计算机断层扫描显示腹膜后肿瘤突出到胸腔,左侧有胸腔积液。肿瘤活检显示肉瘤。我们对肿瘤以及隔膜的一部分进行了完全切除,并用假体补片代替了隔膜。组织病理学结果提示低度纤维粘液样肉瘤。患者无术后并发症,未接受辅助治疗。此外,她在手术后存活了4年,没有复发。
完整的手术切除对低级别纤维粘液样肉瘤有效;因此,当活检显示恶性发现时,适当计划完全切除是很重要的。
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