Abstract:
Juvenile ossifying fibroma (JOF) and its variants, including juvenile psammomatoid ossifying fibroma (JPOF), represent rare yet clinically significant benign fibro-osseous lesions that primarily occur in children and young adolescents. They can be found in diverse anatomical sites such as the jaw, nasal cavity, paranasal sinuses, and orbit. JOF exhibits an aggressive nature, necessitating early radiological detection and surgical intervention. Similarly, JPOF, with a locally malignant potential, requires surgical removal, typically conducted through endoscopic approaches. We report a case of a 5-year-old girl with JPOF arising in the ethmoid, revealed by recurrent epistaxis and proptosis. The text emphasizes the importance of early diagnosis through histopathology as a diagnostic tool and underscores the need for appropriate management.
摘要:
青少年骨化性纤维瘤(JOF)及其变种,包括幼年沙瘤样骨化性纤维瘤(JPOF),代表罕见但具有临床意义的良性纤维骨病变,主要发生在儿童和青少年中。它们可以在不同的解剖部位找到,比如下巴,鼻腔,鼻旁窦,轨道。JOF表现出侵略性,需要早期放射学检测和手术干预。同样,JPOF,具有局部恶性潜能,需要手术切除,通常通过内窥镜方法进行。我们报告了一例5岁女孩在筛骨中出现JPOF,通过复发性鼻出血和眼球突出显示。本文强调了通过组织病理学作为诊断工具进行早期诊断的重要性,并强调了适当管理的必要性。