脂肪酸吸收不良 , 其次是乳糜微粒畸形 ,不是胰腺功能不全,导致囊性纤维化的代谢缺陷。
Mesh : Cystic Fibrosis / metabolism complications Humans Chylomicrons / metabolism Fatty Acids / metabolism Exocrine Pancreatic Insufficiency / metabolism Malabsorption Syndromes / metabolism
来 源:
DOI:10.1016/j.jlr.2024.100549
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