Abstract：
Moyamoya syndrome (MMS) is a rare, chronic, progressive cerebrovascular disorder characterized by stenosis at the apices of the intracranial internal carotid arteries, including the proximal anterior cerebral arteries and middle cerebral arteries. Cerebral angiography images are used for detection through measurement. Systemic lupus erythematosus (SLE) is an autoimmune disease that can cause multisystemic involvement. The coexistence of SLE and MMS has been rarely reported in the literature. A 46-year-old male patient with malar rash, Raynaud phenomenon presented to the hospital with a complaint of weakness in the left lower extremity, which began 3 days before the date of the visit. In the diffusion magnetic resonance imaging, multiple diffusion restrictions were observed in the right frontal region. The patient underwent MR angiography, revealing stenosis in the terminal and supraclinoid segments of the right internal carotid artery, which made us consider moyamoya disease. This patient, with a malar rash and Raynaud\'s, a positive antibody profile, was diagnosed as a male with SLE accompanied by MMS.
摘要：
烟雾综合症（MMS）是一种罕见的，慢性，以颅内颈内动脉尖端狭窄为特征的进行性脑血管疾病，包括大脑前动脉和大脑中动脉。脑血管造影图像用于通过测量进行检测。系统性红斑狼疮（SLE）是一种自身免疫性疾病，可引起多系统受累。SLE和MMS的共存在文献中鲜有报道。一名46岁的男性患者患有黄斑皮疹，雷诺现象出现在医院，主诉左下肢无力，在访问日期前3天开始。在扩散磁共振成像中，在右额叶区域观察到多重扩散限制.患者接受了MR血管造影,在右颈内动脉的末端和上动脉段显示狭窄，这让我们想到了烟雾病。这个病人,有一个Malar皮疹和Raynaud\'s,抗体阳性,被诊断为男性SLE伴MMS。
