PDF(Pubmed)
Abstract：
BACKGROUND: Aneurysmal bone cysts (ABCs) are benign, osteolytic lesions that can occur in long bones, vertebrae, or rarely, the skull. Here the authors present the case of a 15-year-old male with a primary ABC of the left frontoparietal skull along with a review of the literature to provide insight into the nature of this rare disease.
METHODS: An otherwise healthy 15-year-old male presented with a tense, painful lesion of the left frontoparietal scalp. He could not identify any inciting trauma, but first noted the lesion less than 2 weeks prior to presentation with progressive enlargement. Cranial imaging revealed a lytic skull lesion with fluid-fluid levels suggestive of ABC. Curative therapy was provided via wide excision of the lesion and calvarial reconstruction of the resultant skull defect. This was performed without complication, and histopathological evaluation confirmed the diagnosis of primary ABC.
CONCLUSIONS: ABCs of the skull are rare entities and most often arise in the skull base versus the calvaria. Typically, these lesions are associated with an underlying bone pathology (secondary ABCs) but can be rarely seen as isolated lesions (primary ABCs). Clinical management consists of excision and adjuvant therapy for underlying pathology where appropriate.
METHODS: An otherwise healthy 15-year-old male presented with a tense, painful lesion of the left frontoparietal scalp. He could not identify any inciting trauma, but first noted the lesion less than 2 weeks prior to presentation with progressive enlargement. Cranial imaging revealed a lytic skull lesion with fluid-fluid levels suggestive of ABC. Curative therapy was provided via wide excision of the lesion and calvarial reconstruction of the resultant skull defect. This was performed without complication, and histopathological evaluation confirmed the diagnosis of primary ABC.
CONCLUSIONS: ABCs of the skull are rare entities and most often arise in the skull base versus the calvaria. Typically, these lesions are associated with an underlying bone pathology (secondary ABCs) but can be rarely seen as isolated lesions (primary ABCs). Clinical management consists of excision and adjuvant therapy for underlying pathology where appropriate.
摘要：
背景：动脉瘤性骨囊肿（ABCs）是良性的，长骨中可能发生的溶骨性病变，椎骨,或者很少，头骨。在这里，作者介绍了一名15岁男性的左额顶颅骨原发性ABC的病例，并回顾了文献，以深入了解这种罕见疾病的性质。
方法：一名健康的15岁男性表现出紧张，左额顶头皮疼痛病变。他无法识别任何煽动创伤，但在出现前不到2周首先注意到病变逐渐增大。颅骨成像显示颅骨溶解性病变，液体水平提示ABC。通过广泛切除病变并重建颅骨缺损提供治疗。这没有并发症，组织病理学评估证实了原发性ABC的诊断。
结论：颅骨的ABCs是罕见实体，最常见于颅底和颅骨。通常,这些病变与潜在的骨病理学(继发性ABCs)相关,但很少见到孤立性病变(原发性ABCs).临床管理包括切除和适当的基础病理的辅助治疗。
方法：一名健康的15岁男性表现出紧张，左额顶头皮疼痛病变。他无法识别任何煽动创伤，但在出现前不到2周首先注意到病变逐渐增大。颅骨成像显示颅骨溶解性病变，液体水平提示ABC。通过广泛切除病变并重建颅骨缺损提供治疗。这没有并发症，组织病理学评估证实了原发性ABC的诊断。
结论：颅骨的ABCs是罕见实体，最常见于颅底和颅骨。通常,这些病变与潜在的骨病理学(继发性ABCs)相关,但很少见到孤立性病变(原发性ABCs).临床管理包括切除和适当的基础病理的辅助治疗。
