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Abstract：
Gastrointestinal angiosarcoma is an extremely rare malignant tumor of the digestive tract, characterized by a very poor prognosis, with few patients surviving more than 1 year after diagnosis. This case report describes a 71-year-old female patient with a 3-year history of intermittent abdominal pain and significant exacerbation of abdominal pain and bloating 2 weeks prior to treatment. After surgical treatment, the pathological and immunohistochemical diagnosis was primary epithelioid angiosarcoma of the jejunal mesentery. The patient refused postoperative adjuvant chemotherapy and died 4 months after diagnosis due to widespread systemic metastasis. In addition, this article reviews 38 previously reported cases of primary gastrointestinal angiosarcoma, aiming to further understand angiosarcoma and thus guide clinical practitioners in providing more comprehensive treatment approaches.
摘要：
胃肠道血管肉瘤是一种极其罕见的消化道恶性肿瘤，以预后极差为特征，少数患者在诊断后存活超过1年。该病例报告描述了一名71岁的女性患者，有3年的间歇性腹痛病史，并且在治疗前2周出现腹痛和腹胀的明显加重。手术治疗后,病理和免疫组织化学诊断为空肠肠系膜原发性上皮样血管肉瘤。患者拒绝术后辅助化疗，诊断后4个月因全身转移而死亡。此外,本文回顾了以前报道的38例原发性胃肠道血管肉瘤，旨在进一步了解血管肉瘤，从而指导临床医生提供更全面的治疗方法。
