PDF(Pubmed)
Abstract：
UNASSIGNED: Urachal tumors are rare in clinical practice, among which urachal adenocarcinoma is the most common. In this study, we report a rare case of urachal perivascular epithelioid cell tumor to improve our understanding of the disease.
UNASSIGNED: A 26-year-old male patient was hospitalized for lower abdominal pain. The US showed a hypoechoic mass measuring 26mm × 18mm in the superior aspect of the bladder. MRI showed an irregular mass located anterior to the bladder roof, near the midline. The tumor exhibited hypointense on T1WI and heterogeneous hyperintense on T2WI. Additionally, contrast-enhanced T1-weighted imaging revealed obvious ring enhancement of the tumor. The patient underwent surgical resection of the urachal tumor, with subsequent pathological examination revealing a diagnosis of urachal PEComa. Following surgery, the patient underwent regular follow-up assessments, with no evidence of recurrence or metastasis observed after three and a half years.
UNASSIGNED: Urachal PEComa is a rare mesenchymal tumor that presents challenges in diagnosis through imaging and clinical symptoms. Definitive diagnosis relies on pathological and immunohistochemical analysis. Due to the rarity of urachal PEComa, prognosis assessment necessitates long-term follow-up and evaluation of more cases.
UNASSIGNED: A 26-year-old male patient was hospitalized for lower abdominal pain. The US showed a hypoechoic mass measuring 26mm × 18mm in the superior aspect of the bladder. MRI showed an irregular mass located anterior to the bladder roof, near the midline. The tumor exhibited hypointense on T1WI and heterogeneous hyperintense on T2WI. Additionally, contrast-enhanced T1-weighted imaging revealed obvious ring enhancement of the tumor. The patient underwent surgical resection of the urachal tumor, with subsequent pathological examination revealing a diagnosis of urachal PEComa. Following surgery, the patient underwent regular follow-up assessments, with no evidence of recurrence or metastasis observed after three and a half years.
UNASSIGNED: Urachal PEComa is a rare mesenchymal tumor that presents challenges in diagnosis through imaging and clinical symptoms. Definitive diagnosis relies on pathological and immunohistochemical analysis. Due to the rarity of urachal PEComa, prognosis assessment necessitates long-term follow-up and evaluation of more cases.
摘要：
■Urachal肿瘤在临床实践中很少见，其中脐尿管腺癌最为常见。在这项研究中,我们报道了一例罕见的脐尿管血管周围上皮样细胞瘤，以提高我们对该疾病的认识。
■一名26岁男性患者因下腹痛住院。美国在膀胱上部显示出26mm×18mm的低回声肿块。MRI显示膀胱顶部前方有不规则肿块，在中线附近。肿瘤在T1WI上表现为低信号，在T2WI上表现为异质性高信号。此外,对比增强T1加权成像显示肿瘤明显的环形增强。患者接受了脐静脉肿瘤的手术切除,随后的病理检查显示诊断为脐尿管PEComa。手术后,患者接受定期随访评估，三年半后没有观察到复发或转移的证据。
■UrachalPEComa是一种罕见的间叶性肿瘤，通过影像学和临床症状对诊断提出了挑战。明确的诊断依赖于病理和免疫组织化学分析。由于脐带血PEComa的罕见，预后评估需要长期随访和评估更多病例。
■一名26岁男性患者因下腹痛住院。美国在膀胱上部显示出26mm×18mm的低回声肿块。MRI显示膀胱顶部前方有不规则肿块，在中线附近。肿瘤在T1WI上表现为低信号，在T2WI上表现为异质性高信号。此外,对比增强T1加权成像显示肿瘤明显的环形增强。患者接受了脐静脉肿瘤的手术切除,随后的病理检查显示诊断为脐尿管PEComa。手术后,患者接受定期随访评估，三年半后没有观察到复发或转移的证据。
■UrachalPEComa是一种罕见的间叶性肿瘤，通过影像学和临床症状对诊断提出了挑战。明确的诊断依赖于病理和免疫组织化学分析。由于脐带血PEComa的罕见，预后评估需要长期随访和评估更多病例。
