Abstract：
Despite distinct diagnostic criteria, several gastrointestinal pathologies can masquerade haemophagocytic lymphohistiocytosis (HLH) during the peripartum period. Acute fatty liver of pregnancy, HELLP (haemolysis, elevated liver enzymes and low platelets) syndrome, miliary tuberculosis, visceral leishmaniasis, abdominal surgical emergencies, haemolytic anaemias and haematological malignancies may have clinical and laboratory presentation similar to that of HLH. In this report, we present the case of a 26-year-old woman with 38-weeks\' gestation and abdominal pain, vomiting, intermittent fever and non-productive cough for 1-2 months. A thorough investigation suggested HLH and the patient was successfully treated with corticosteroids. This patient demonstrates the importance of a focused investigation strategy and timely management to prevent mortality and morbidity to both the mother and fetus in this rare and fatal disease.
摘要：
尽管有不同的诊断标准，在围产期，几种胃肠道疾病可以掩盖噬血细胞性淋巴组织细胞增多症（HLH）。妊娠急性脂肪肝,HELLP（溶血，肝酶升高和低血小板）综合征，粟粒性肺结核,内脏利什曼病，腹部外科急症,溶血性贫血和血液系统恶性肿瘤的临床和实验室表现可能与HLH相似。在这份报告中,我们介绍了一个26岁的女性，妊娠38周，腹痛，呕吐,间歇性发热和非生产性咳嗽1-2个月。彻底的调查显示HLH，患者成功接受了皮质类固醇治疗。该患者证明了在这种罕见且致命的疾病中，有针对性的调查策略和及时管理以防止母亲和胎儿死亡和发病的重要性。
