Abstract：
METHODS: We describe the surgical management of a girl with dwarfism and congenital spondyloepiphyseal dysplasia, who presented in adolescence with coxa vara and bilateral pseudarthrosis between the femoral neck and the diaphysis, with asymmetric distal migration at both sites and leg length discrepancy. The patient at 16 years underwent valgus osteotomy in situ and femoral neck fixation in the left hip. The right hip was operated 19 months later.
CONCLUSIONS: Hip dysplasia is common in spondyloepiphyseal dysplasia, but a debilitating nontraumatic bilateral pseudarthrosis at the base of the femoral neck has not been previously reported. Valgus corrective osteotomies of the femur in situ led to union and allowed the patient to walk.
CONCLUSIONS: Hip dysplasia is common in spondyloepiphyseal dysplasia, but a debilitating nontraumatic bilateral pseudarthrosis at the base of the femoral neck has not been previously reported. Valgus corrective osteotomies of the femur in situ led to union and allowed the patient to walk.
摘要：
方法：我们描述了一个患有侏儒症和先天性脊柱骨发育不良的女孩的手术治疗，在青春期出现髋内翻和股骨颈和骨干之间的双侧假关节，在两个部位和腿长差异的不对称远端迁移。16岁的患者接受了外翻原位截骨术和左髋股骨颈固定术。19个月后进行右髋关节手术。
结论：髋关节发育不良常见于脊椎骨骨发育不良，但是以前没有报道过股骨颈底部的非创伤性双侧假关节衰弱。股骨外翻矫正性原位截骨术导致愈合并允许患者行走。
结论：髋关节发育不良常见于脊椎骨骨发育不良，但是以前没有报道过股骨颈底部的非创伤性双侧假关节衰弱。股骨外翻矫正性原位截骨术导致愈合并允许患者行走。
