PDF(Pubmed)
Abstract：
Cavernous hemangiomas occur most commonly in the cerebral hemispheres but can involve any part of the neuroaxis, including the spine. Very rare cases of spinal angiomas are associated with a skin lesion in the same metameric segment. This condition, known as segmental neurovascular syndrome or Cobb syndrome, was first described in 1915. We report a rare case of segmental neurovascular syndrome with extensive cervical and thoracic lumbar involvement expressed as peripartum spinal cord compression syndrome. A 37-year-old female with a cutaneous nevus from the C7 dermatome to the L3 dermatome experienced pelvic limb paralysis 48 hours after giving birth to a healthy newborn by cesarean section. Magnetic resonance imaging (MRI) revealed an enhancing extensive epidural mass from C7 to T7 and subsequently from T10 to L3. Histopathology confirmed a spinal cavernous hemangioma. Although rare, segmental neurovascular syndrome must be considered in patients with cutaneous angioma and radiculopathy or myelopathy. Early diagnosis can lead to curative surgical treatment and more favorable outcomes.
摘要：
海绵状血管瘤最常见于大脑半球，但可累及神经轴的任何部分。包括脊柱。非常罕见的脊髓血管瘤病例与同一同分异构体中的皮肤病变有关。这个条件,被称为节段性神经血管综合征或Cobb综合征，最早描述于1915年。我们报告了一例罕见的节段性神经血管综合征，伴有广泛的颈和胸腰椎受累，表现为围产期脊髓压迫综合征。一名37岁的女性，从C7皮刀到L3皮刀有皮肤痣，在剖腹产生下健康新生儿48小时后，经历了盆腔肢体瘫痪。磁共振成像（MRI）显示，从C7到T7以及随后从T10到L3的硬膜外肿块增强。组织病理学证实为脊髓海绵状血管瘤。虽然罕见，对于皮肤血管瘤和神经根病或脊髓病患者，必须考虑节段性神经血管综合征。早期诊断可以导致治愈性手术治疗和更有利的结果。
