PDF(Pubmed)
Abstract：
UNASSIGNED: This study examines the value of a new alphanumerical documentation system to classify the whole spectrum of deformities in ulnar longitudinal deficiency (ULD).
UNASSIGNED: The patients with ULD, whom were referred during a 35-year period, were identified from the hospital database. A total of 7 patients with photographs and/or conventional radiographs that could be adequately reproduced were enrolled in the study.
UNASSIGNED: Six patients could be classified with the previously proposed classifications and the new documentation system. Three of them were diagnosed with ulnar-deficient hands. One had aplasia of the fifth finger ray (phalanges and metacarpal), a second aplasia of the fourth and fifth finger rays with narrowing of the first web, and a third aplasia of the fifth metacarpal. Furthermore, a fourth patient was diagnosed with hypoplasia of the ulna and congenital wrist amputation; a fifth with hypoplasia of the ulna, dislocation of the radial head, and a bowed radius; and a sixth with partial aplasia involving the middle and distal diaphysis of the ulna. Finally, one patient with an absent ulnar styloid process and oligodactyly with thumb could be classified only with the new system.
UNASSIGNED: The proposed new alphanumerical documentation system incorporates all the most widely accepted previous classification schemes, facilitates the morphological and radiographic description of the whole spectrum of the deformities detected in patients with ULD for better communication between scientists, and secures the unrestricted inclusion of new variants in the future.
UNASSIGNED: The patients with ULD, whom were referred during a 35-year period, were identified from the hospital database. A total of 7 patients with photographs and/or conventional radiographs that could be adequately reproduced were enrolled in the study.
UNASSIGNED: Six patients could be classified with the previously proposed classifications and the new documentation system. Three of them were diagnosed with ulnar-deficient hands. One had aplasia of the fifth finger ray (phalanges and metacarpal), a second aplasia of the fourth and fifth finger rays with narrowing of the first web, and a third aplasia of the fifth metacarpal. Furthermore, a fourth patient was diagnosed with hypoplasia of the ulna and congenital wrist amputation; a fifth with hypoplasia of the ulna, dislocation of the radial head, and a bowed radius; and a sixth with partial aplasia involving the middle and distal diaphysis of the ulna. Finally, one patient with an absent ulnar styloid process and oligodactyly with thumb could be classified only with the new system.
UNASSIGNED: The proposed new alphanumerical documentation system incorporates all the most widely accepted previous classification schemes, facilitates the morphological and radiographic description of the whole spectrum of the deformities detected in patients with ULD for better communication between scientists, and secures the unrestricted inclusion of new variants in the future.
摘要：
■这项研究检查了一种新的字母数字文档系统的价值，该系统可对尺骨纵向缺陷（ULD）中畸形的整个频谱进行分类。
■ULD患者，他们在35年的时间里被转介，是从医院数据库中识别出来的。共有7名具有可以充分再现的照片和/或常规X射线照片的患者被纳入研究。
■可以使用先前提出的分类和新的文件系统对6名患者进行分类。其中三人被诊断为尺骨缺乏症。其中一人第五指线(指骨和掌骨)发育不全，随着第一幅网的变窄，第四和第五手指射线的第二次再生，和第五掌骨的第三次发育不全。此外，第四例患者被诊断为尺骨发育不全和先天性腕部截肢；五分之一的尺骨发育不全，桡骨头的错位,桡骨弯曲；第六例部分发育不全，涉及尺骨中段和远端骨干。最后,一名尺骨茎突缺失且拇指少指的患者只能使用新系统进行分类。
■拟议的新字母数字文档系统包含了所有最广泛接受的先前分类方案，有助于对ULD患者中检测到的畸形的整个光谱进行形态学和放射学描述，以便科学家之间更好地进行交流，并确保未来不受限制地包含新的变体。
■ULD患者，他们在35年的时间里被转介，是从医院数据库中识别出来的。共有7名具有可以充分再现的照片和/或常规X射线照片的患者被纳入研究。
■可以使用先前提出的分类和新的文件系统对6名患者进行分类。其中三人被诊断为尺骨缺乏症。其中一人第五指线(指骨和掌骨)发育不全，随着第一幅网的变窄，第四和第五手指射线的第二次再生，和第五掌骨的第三次发育不全。此外，第四例患者被诊断为尺骨发育不全和先天性腕部截肢；五分之一的尺骨发育不全，桡骨头的错位,桡骨弯曲；第六例部分发育不全，涉及尺骨中段和远端骨干。最后,一名尺骨茎突缺失且拇指少指的患者只能使用新系统进行分类。
■拟议的新字母数字文档系统包含了所有最广泛接受的先前分类方案，有助于对ULD患者中检测到的畸形的整个光谱进行形态学和放射学描述，以便科学家之间更好地进行交流，并确保未来不受限制地包含新的变体。
