PDF(Pubmed)
Abstract：
Median arcuate ligament syndrome (MALS) is a rare clinical entity arising from the extrinsic compression of the coeliac axis by the median arcuate ligament. In this report, we detail a unique presentation involving monozygotic twins, both of whom demonstrated anatomical extrinsic compression of the coeliac axis by the median arcuate ligament. Intriguingly, only one twin manifested clinical symptoms consistent with MALS, despite comparable anatomical compression of the coeliac axis observed in both. This case highlights the potential interplay of a genetic or anatomical predisposition to coeliac axis compression and secondary, possibly environmental, factors that lead to the development of clinical symptoms. In this report, we explore various determinants potentially influencing symptomatology in MALS and advocate for the publication of similar case studies to further elucidate this rare condition.
摘要：
正中弓状韧带综合征（MALS）是一种罕见的临床实体，由正中弓状韧带对腹腔轴的外部压迫引起。在这份报告中,我们详细介绍了一个涉及单卵双胞胎的独特表现，两人都表现出正中弓状韧带对腹腔轴的解剖外在压迫。有趣的是，只有一个双胞胎表现出与MALS一致的临床症状，尽管在两者中观察到乳糜轴的解剖压缩相当。这种情况突出了遗传或解剖学倾向的潜在相互作用，以腹腔轴压缩和继发性，可能是环境,导致临床症状发展的因素。在这份报告中,我们探索了可能影响MALS症状学的各种决定因素,并倡导发表类似的案例研究,以进一步阐明这种罕见的情况.
