Abstract:
Diffuse abdominal lymphangiomatosis is a rare and complex disease. It typically presents with non-specific gastrointestinal symptoms and characteristic cystic lesions or tumoral masses on imaging based on the literature to date. This report presents the rare case of a young man with an atypical form of diffuse abdominal lymphangiomatosis in the complete absence of cystic lesions or lymphangioma tumoral masses, thus presenting a unique diagnostic challenge. It was successively treated by surgery, gastric electrical stimulator, sirolimus, and imatinib.
摘要:
弥漫性腹部淋巴管瘤病是一种罕见且复杂的疾病。根据迄今为止的文献,它通常表现为非特异性胃肠道症状和特征性囊性病变或肿瘤肿块。本报告介绍了一例罕见的年轻人,患有非典型形式的弥漫性腹部淋巴管瘤病,完全没有囊性病变或淋巴管瘤肿瘤肿块。因此提出了独特的诊断挑战。先后经过手术治疗,胃电刺激器,西罗莫司,还有伊马替尼.