Abstract：
The term \'sclerosing diseases of the skin\' comprises specific dermatological entities, which have fibrotic changes of the skin in common. These diseases mostly manifest in different clinical subtypes according to cutaneous and extracutaneous involvement and can sometimes be difficult to distinguish from each other. The present consensus provides an update to the 2017 European Dermatology Forum Guidelines, focusing on characteristic clinical and histopathological features, diagnostic scores and the serum autoantibodies most useful for differential diagnosis. In addition, updated strategies for the first- and advanced-line therapy of sclerosing skin diseases are addressed in detail. Part 2 of this consensus provides clinicians with an overview of the diagnosis and treatment of scleromyxoedema and scleroedema (of Buschke).
摘要：
术语“皮肤硬化性疾病”包括特定的皮肤病学实体，有共同的皮肤纤维化变化。根据皮肤和皮外受累，这些疾病大多表现为不同的临床亚型，有时很难区分。本共识提供了对2017年欧洲皮肤病学论坛指南的更新。关注特征性临床和组织病理学特征，诊断评分和血清自身抗体对鉴别诊断最有用。此外,详细介绍了硬化性皮肤病一线和高级治疗的最新策略。该共识的第2部分为临床医生提供了巩膜粘水肿和硬化性水肿（Buschke）的诊断和治疗概述。
