PDF(Pubmed)
Abstract：
Lymphatic malformations (LMs) are one of the congenital malformations of the lymphatic system in the body. The patient usually presents with head and neck swelling, airway compression, and/or airway obstruction. The diagnosis of retropharyngeal LMs can be challenging due to their rare occurrence. We report a case of a five-month-old boy diagnosed with retropharyngeal LMs. He presented with a three-day history of fever, cough, and stridor and was initially treated for acute bronchiolitis. A lateral neck radiograph revealed prevertebral widening, suggesting retropharyngeal collection. The patient\'s condition worsened, requiring intubation in the operating room and proceeding with aspirations and drainage. However, the symptoms recurred after a few days, necessitating re-intubation, repeated aspirations and drainage procedures. The patient was intubated, and the neck\'s magnetic resonance imaging (MRI) confirmed retropharyngeal LMs. An elective tracheostomy was performed and was treated with sirolimus. The patient had a successful tracheostomy decannulation and showed no recurrence during follow-up.
摘要：
淋巴畸形（LMs）是人体淋巴系统的先天性畸形之一。患者通常表现为头颈部肿胀，气道压缩,和/或气道阻塞。咽后LMs的诊断由于其罕见的发生而具有挑战性。我们报告了一个5个月大的男孩被诊断患有咽后LMs的病例。他有三天的发烧史，咳嗽,和喘鸣，最初治疗急性细支气管炎。颈部侧位X线片显示椎体前加宽，建议咽后收集。病人的病情恶化了,需要在手术室插管，并进行抽吸和引流。然而,几天后症状复发，需要重新插管，重复的愿望和排水程序。病人被插管,颈部磁共振成像（MRI）证实咽后LMs。进行了选择性气管造口术，并接受了西罗莫司治疗。该患者成功进行了气管造口术，并且在随访期间没有复发。
