PDF(Pubmed)
Abstract：
BACKGROUND: Chondrosarcoma is an uncommon spinal tumor that can present as an extraskeletal mass. Rarely, these tumors present as dumbbell tumors through the neural foramina, mimicking schwannomas or neurofibromas.
METHODS: A 46-year-old female presented with 2 years of worsening right-arm radiculopathy. Magnetic resonance imaging of the thoracic spine revealed a peripherally enhancing extramedullary mass through the right T1 foramen and compressing the spinal cord. Computed tomography showed the mass to be partially calcified. She underwent C7-T2 laminectomy and C6-T3 posterior instrumented fusion with gross-total resection of an extradural mass. Pathology revealed a grade I chondrosarcoma. Her symptoms improved postoperatively, with some residual right-arm radicular pain.
CONCLUSIONS: Intraspinal extradural dumbbell conventional chondrosarcoma is rare, with only 9 cases, including ours, reported. Patient ages range from 16 to 72 years old, and male sex is more common in these cases. The most common location is the thoracic spine, and our case is the only reported one in the cervicothoracic junction. These tumors often mimic schwannomas on imaging, but chondrosarcoma should remain in the differential diagnosis, because management of these tumors differs. Chondrosarcoma may benefit from more aggressive resection, including en bloc resection, and may require adjuvant radiotherapy.
METHODS: A 46-year-old female presented with 2 years of worsening right-arm radiculopathy. Magnetic resonance imaging of the thoracic spine revealed a peripherally enhancing extramedullary mass through the right T1 foramen and compressing the spinal cord. Computed tomography showed the mass to be partially calcified. She underwent C7-T2 laminectomy and C6-T3 posterior instrumented fusion with gross-total resection of an extradural mass. Pathology revealed a grade I chondrosarcoma. Her symptoms improved postoperatively, with some residual right-arm radicular pain.
CONCLUSIONS: Intraspinal extradural dumbbell conventional chondrosarcoma is rare, with only 9 cases, including ours, reported. Patient ages range from 16 to 72 years old, and male sex is more common in these cases. The most common location is the thoracic spine, and our case is the only reported one in the cervicothoracic junction. These tumors often mimic schwannomas on imaging, but chondrosarcoma should remain in the differential diagnosis, because management of these tumors differs. Chondrosarcoma may benefit from more aggressive resection, including en bloc resection, and may require adjuvant radiotherapy.
摘要：
背景：软骨肉瘤是一种罕见的脊柱肿瘤，可表现为骨外肿块。很少,这些肿瘤通过神经孔表现为哑铃状肿瘤，模仿神经鞘瘤或神经纤维瘤。
方法：一名46岁女性，表现为右臂神经根病恶化2年。胸椎的磁共振成像显示，通过右T1孔并压迫脊髓的外周增强的髓外肿块。计算机断层扫描显示肿块部分钙化。她接受了C7-T2椎板切除术和C6-T3后路器械融合，并全切了硬膜外肿块。病理显示为I级软骨肉瘤。她的症状在术后好转,有一些残留的右臂神经根疼痛。
结论：椎管内硬膜外哑铃型常规软骨肉瘤少见，只有9个案例，包括我们的,报告。患者年龄从16岁到72岁，男性在这些病例中更为常见。最常见的位置是胸椎，我们的病例是颈胸交界处唯一的病例.这些肿瘤通常在成像上模仿神经鞘瘤，但是软骨肉瘤应该保留在鉴别诊断中，因为这些肿瘤的管理方式不同。软骨肉瘤可能受益于更积极的切除，包括整块切除,可能需要辅助放疗。
方法：一名46岁女性，表现为右臂神经根病恶化2年。胸椎的磁共振成像显示，通过右T1孔并压迫脊髓的外周增强的髓外肿块。计算机断层扫描显示肿块部分钙化。她接受了C7-T2椎板切除术和C6-T3后路器械融合，并全切了硬膜外肿块。病理显示为I级软骨肉瘤。她的症状在术后好转,有一些残留的右臂神经根疼痛。
结论：椎管内硬膜外哑铃型常规软骨肉瘤少见，只有9个案例，包括我们的,报告。患者年龄从16岁到72岁，男性在这些病例中更为常见。最常见的位置是胸椎，我们的病例是颈胸交界处唯一的病例.这些肿瘤通常在成像上模仿神经鞘瘤，但是软骨肉瘤应该保留在鉴别诊断中，因为这些肿瘤的管理方式不同。软骨肉瘤可能受益于更积极的切除，包括整块切除,可能需要辅助放疗。
