PDF(Pubmed)
Abstract：
UNASSIGNED: Pseudomyxoma peritonei (PMP) is a clinical entity of subtle onset abdominal pain, ascites, and distention associated with characteristic imaging. In most cases, laparoscopic exploration will give the definitive diagnosis and histopathologic verification. However, usually there are difficulties in the diagnosis of this disease.
UNASSIGNED: Herein, we present a case of a 51-year-old female who developed ascites over 5 months. An investigational laparotomy established the diagnosis of PMP, after the discovery of a mucinous, grey-brown tumor that was CK20 positive and CK7 negative. Subsequently, chemotherapy with oxaliplatin combined with 5-FU (FOLFOX4 regimen), was initiated and the patient survived for 30 months. We also present a comprehensive review of the English literature concerning the different symptoms and radiological findings of this rare entity. According to the literature review, 35 cases of PMP with different clinical and radiological findings have been described. In the majority of the cases, ultrasound, computed tomography or magnetic resonance imaging was orientating towards a proper diagnosis before a diagnostic laparotomy.
UNASSIGNED: The combination of a clinical picture with the characteristic imaging findings enables a prompt diagnosis of PMP, making prognosis more favorable.
UNASSIGNED: Herein, we present a case of a 51-year-old female who developed ascites over 5 months. An investigational laparotomy established the diagnosis of PMP, after the discovery of a mucinous, grey-brown tumor that was CK20 positive and CK7 negative. Subsequently, chemotherapy with oxaliplatin combined with 5-FU (FOLFOX4 regimen), was initiated and the patient survived for 30 months. We also present a comprehensive review of the English literature concerning the different symptoms and radiological findings of this rare entity. According to the literature review, 35 cases of PMP with different clinical and radiological findings have been described. In the majority of the cases, ultrasound, computed tomography or magnetic resonance imaging was orientating towards a proper diagnosis before a diagnostic laparotomy.
UNASSIGNED: The combination of a clinical picture with the characteristic imaging findings enables a prompt diagnosis of PMP, making prognosis more favorable.
摘要：
■腹膜假粘液瘤（PMP）是一种轻微发作的腹痛的临床实体，腹水,以及与特征性成像相关的扩张。在大多数情况下,腹腔镜探查将提供明确的诊断和组织病理学验证。然而,这种疾病的诊断通常有困难。
■这里，我们介绍了一例51岁女性，她在5个月内出现腹水。一项研究性剖腹手术确定了PMP的诊断，在发现粘液后，灰褐色肿瘤，CK20阳性，CK7阴性。随后，奥沙利铂联合5-FU（FOLFOX4方案）化疗，开始，患者存活30个月。我们还对有关这种罕见实体的不同症状和放射学发现的英文文献进行了全面回顾。根据文献综述,已描述了35例具有不同临床和放射学发现的PMP。在大多数情况下,超声，在诊断性剖腹手术之前,计算机断层扫描或磁共振成像正朝着正确的诊断方向发展.
■将临床表现与特征性影像学表现相结合，可以迅速诊断PMP，使预后更有利。
■这里，我们介绍了一例51岁女性，她在5个月内出现腹水。一项研究性剖腹手术确定了PMP的诊断，在发现粘液后，灰褐色肿瘤，CK20阳性，CK7阴性。随后，奥沙利铂联合5-FU（FOLFOX4方案）化疗，开始，患者存活30个月。我们还对有关这种罕见实体的不同症状和放射学发现的英文文献进行了全面回顾。根据文献综述,已描述了35例具有不同临床和放射学发现的PMP。在大多数情况下,超声，在诊断性剖腹手术之前,计算机断层扫描或磁共振成像正朝着正确的诊断方向发展.
■将临床表现与特征性影像学表现相结合，可以迅速诊断PMP，使预后更有利。
