Abstract：
Neurosynovial tumors, originating from Schwann cells within nerve sheaths, are benign entities, with 25% to 45% manifesting in the head and neck region. However, occurrences in the pterygopalatine fossa (PPF) are exceptionally rare, and only a handful of cases have been documented. In this report, we present the unique case of a 6-year-old child exhibiting a sizable soft tissue mass in the left PPF, extending into the inferior orbital fissure. The patient underwent successful intranasal endoscopic removal of PPF schwannoma utilizing the prelacrimal recess approach, with postoperative pathology confirming the diagnosis of schwannoma. Schwannomas within the PPF are particularly uncommon, and instances of such tumors in pediatric patients are even more exceptional. This case highlights the diagnostic and therapeutic challenges associated with PPF schwannomas in children, emphasizing the significance of a multidisciplinary approach for optimal management. In addition, a comprehensive literature review is presented to provide insights into the existing knowledge on this rare entity, further contributing to the understanding of pediatric PPF schwannomas.
摘要：
神经滑膜肿瘤,源自神经鞘内的施万细胞,是良性实体，25%到45%出现在头颈部。然而,翼腭窝（PPF）的发生非常罕见，只有少数案例被记录在案。在这份报告中,我们介绍了一个6岁儿童在左侧PPF表现出相当大的软组织肿块的独特病例，延伸到下眶裂缝。患者通过泪前隐窝入路成功经鼻内镜切除PPF神经鞘瘤，术后病理证实神经鞘瘤的诊断。PPF内的神经鞘瘤特别罕见，儿科患者中这种肿瘤的情况甚至更加特殊。该病例强调了与儿童PPF神经鞘瘤相关的诊断和治疗挑战。强调多学科方法对优化管理的重要性。此外,提出了一个全面的文献综述，以提供对这个罕见实体的现有知识的见解，进一步有助于理解小儿PPF神经鞘瘤。
