Abstract：
BACKGROUND: Juvenile Psammomatoid Ossifying Fibroma (JPOF) is a type of noncancerous bone tumor that usually affects adolescents in the craniomaxillofacial area. Clinical manifestations are usually symptoms caused by the tumor\'s invasive compression of surrounding tissues. Aneurysmal Bone Cyst (ABC) is also a benign bone tumor, and it typically occurs in long bones and the spine. Only 2% to 3% of cases occur in the head and neck. Due to the rarity of this combination of clinical cases, clinicians face difficulties in comprehensively understanding this complex lesion. Therefore, a comprehensive review of the clinical manifestations and characteristic imaging findings is necessary for surgeons.
METHODS: On April 6, 2019, a 13-year-old boy presented with left maxillofacial bulge and pain for 1 month. Magnetic resonance imaging of the paranasal sinuses showed an irregular hive-like mass signal in the left maxillary sinus, and cystic changes with fluid levels were seen in the lesion. After the initial diagnosis of JPOF with primary ABC, we decided to perform a facial mid-facial resection of maxillary sinus tumor to remove the tumor tissue. Finally, after 3 recurrences and 4 operations, there was no tumor recurrence for 20 months after the last operation, and the patient was still under continuous follow-up.
CONCLUSIONS: This case provided a reference for the diagnosis and treatment of JPOF combined with ABC. In particular, a new understanding of the association between the two diseases and the management of recurrence were proposed, which had the potential to improve clinical understanding of this complicated condition.
METHODS: On April 6, 2019, a 13-year-old boy presented with left maxillofacial bulge and pain for 1 month. Magnetic resonance imaging of the paranasal sinuses showed an irregular hive-like mass signal in the left maxillary sinus, and cystic changes with fluid levels were seen in the lesion. After the initial diagnosis of JPOF with primary ABC, we decided to perform a facial mid-facial resection of maxillary sinus tumor to remove the tumor tissue. Finally, after 3 recurrences and 4 operations, there was no tumor recurrence for 20 months after the last operation, and the patient was still under continuous follow-up.
CONCLUSIONS: This case provided a reference for the diagnosis and treatment of JPOF combined with ABC. In particular, a new understanding of the association between the two diseases and the management of recurrence were proposed, which had the potential to improve clinical understanding of this complicated condition.
摘要：
背景：青少年沙瘤样骨化纤维瘤（JPOF）是一种非癌性骨肿瘤，通常影响青少年的颅颌面区域。临床表现通常是肿瘤侵袭性压迫周围组织引起的症状。动脉瘤性骨囊肿（ABC）也是一种良性骨肿瘤，它通常发生在长骨和脊柱中。只有2％至3％的病例发生在头颈部。由于这种临床病例的罕见，临床医生在全面了解这一复杂病变方面面临困难.因此,对于外科医生来说，全面审查临床表现和特征性影像学表现是必要的。
方法：2019年4月6日，一名13岁男孩出现左侧颌面隆起和疼痛1个月。鼻旁窦的磁共振成像显示左上颌窦有不规则的蜂巢样肿块信号，和囊性改变与液体水平在病变中可见。初次ABC诊断为JPOF后，我们决定对上颌窦肿瘤进行面部中面部切除术以切除肿瘤组织。最后,经过3次复发和4次操作，最后一次手术后20个月没有肿瘤复发，患者仍在持续随访中。
结论：该病例为JPOF合并ABC的诊断和治疗提供了参考。特别是,提出了对这两种疾病之间的关联和复发管理的新认识，这有可能提高临床对这种复杂疾病的认识。
方法：2019年4月6日，一名13岁男孩出现左侧颌面隆起和疼痛1个月。鼻旁窦的磁共振成像显示左上颌窦有不规则的蜂巢样肿块信号，和囊性改变与液体水平在病变中可见。初次ABC诊断为JPOF后，我们决定对上颌窦肿瘤进行面部中面部切除术以切除肿瘤组织。最后,经过3次复发和4次操作，最后一次手术后20个月没有肿瘤复发，患者仍在持续随访中。
结论：该病例为JPOF合并ABC的诊断和治疗提供了参考。特别是,提出了对这两种疾病之间的关联和复发管理的新认识，这有可能提高临床对这种复杂疾病的认识。
