PDF(Pubmed)
Abstract：
BACKGROUND: Intestinal malrotation is an infrequent congenital anomaly primarily observed in neonates, and adult-onset cases are exceedingly rare. Studies on adult congenital intestinal malrotation are limited.
METHODS: A case with congenital intestinal malrotation is reported in our study. The clinical data were collected and the treatment process and effect were evaluated.
RESULTS: A 45-year-old female who had been experiencing vomiting for over 40 years was admitted to our hospital. According to the result of CT scan, intestinal volvulus accompanied by bowel obstruction was suspected. Then laparoscopic examination was applied to the patient and was ultimately diagnosed with adult congenital intestinal malrotation. We performed Ladd\'s procedure combined with gastrojejunostomy and Braun anastomosis. The patient recovered well and was successfully discharged from the hospital on the 13th day after surgery. After a 6-month follow-up, the symptom of vomiting was significantly alleviated and body weight was gained for 10 kg. She was very satisfied with the treatment.
CONCLUSIONS: Adult congenital intestinal malrotation is a rare disease that is often misdiagnosed owing to nonspecific clinical manifestations. Therefore, awareness about this condition should be enhanced. Surgery remains the cornerstone of treatment for this disease. Combining gastrojejunostomy and Braun anastomosis with the traditional Ladd procedure can optimize surgical outcomes.
METHODS: A case with congenital intestinal malrotation is reported in our study. The clinical data were collected and the treatment process and effect were evaluated.
RESULTS: A 45-year-old female who had been experiencing vomiting for over 40 years was admitted to our hospital. According to the result of CT scan, intestinal volvulus accompanied by bowel obstruction was suspected. Then laparoscopic examination was applied to the patient and was ultimately diagnosed with adult congenital intestinal malrotation. We performed Ladd\'s procedure combined with gastrojejunostomy and Braun anastomosis. The patient recovered well and was successfully discharged from the hospital on the 13th day after surgery. After a 6-month follow-up, the symptom of vomiting was significantly alleviated and body weight was gained for 10 kg. She was very satisfied with the treatment.
CONCLUSIONS: Adult congenital intestinal malrotation is a rare disease that is often misdiagnosed owing to nonspecific clinical manifestations. Therefore, awareness about this condition should be enhanced. Surgery remains the cornerstone of treatment for this disease. Combining gastrojejunostomy and Braun anastomosis with the traditional Ladd procedure can optimize surgical outcomes.
摘要：
背景：肠旋转不良是一种罕见的先天性异常，主要在新生儿中观察到，成人发病病例极为罕见。成人先天性肠旋转不良的研究有限。
方法：本研究报告一例先天性肠旋转不良。收集临床资料,评价治疗过程和效果。
结果：一名45岁女性患者呕吐超过40年，入院治疗。根据CT扫描的结果,怀疑肠扭转伴有肠梗阻。然后对患者进行腹腔镜检查，最终诊断为成人先天性肠旋转不良。我们进行了Ladd's手术联合胃空肠吻合术和Braun吻合术。患者恢复良好,术后第13天顺利出院。经过6个月的随访，呕吐症状明显减轻，体重增加10公斤。她对治疗非常满意。
结论：成人先天性肠旋转不良是一种罕见的疾病，常因非特异性临床表现而误诊。因此,应该增强对这种情况的认识。手术仍然是治疗这种疾病的基石。将胃空肠吻合术和Braun吻合术与传统的Ladd手术相结合可以优化手术效果。
方法：本研究报告一例先天性肠旋转不良。收集临床资料,评价治疗过程和效果。
结果：一名45岁女性患者呕吐超过40年，入院治疗。根据CT扫描的结果,怀疑肠扭转伴有肠梗阻。然后对患者进行腹腔镜检查，最终诊断为成人先天性肠旋转不良。我们进行了Ladd's手术联合胃空肠吻合术和Braun吻合术。患者恢复良好,术后第13天顺利出院。经过6个月的随访，呕吐症状明显减轻，体重增加10公斤。她对治疗非常满意。
结论：成人先天性肠旋转不良是一种罕见的疾病，常因非特异性临床表现而误诊。因此,应该增强对这种情况的认识。手术仍然是治疗这种疾病的基石。将胃空肠吻合术和Braun吻合术与传统的Ladd手术相结合可以优化手术效果。
