关键词: ABC Aneurysmal bone cyst MRI

Mesh : Humans Female Bone Cysts, Aneurysmal / surgery diagnostic imaging Adolescent Optic Neuritis / diagnostic imaging Magnetic Resonance Imaging Diagnosis, Differential

来  源:   DOI:10.1007/s00381-024-06283-1

Abstract:
BACKGROUND: Aneurysmal bone cyst (ABC) is an uncommon, benign, vascular multicystic bony lesion that most frequently develops in the first two decades of life. The metaphysis of long bones, pelvic, and vertebral column are the most common locations. The precise underlying pathophysiology of ABCs formation remains unclear; however, it is believed that reactive processes subsequent to trauma or vascular disturbance may play an important role. Involvement of the skull base rarely occurs with a prevalence of up to 5% of intracranial ABCs.
METHODS: An 18-year-old adolescent female with a history of progressive blurred vision since three months ago presented to our office. The brain and orbital MRI demonstrated no abnormal findings. After three months of glucocorticoid treatment with the diagnosis of multiple sclerosis, the visual impairment of the left eye deteriorated abruptly. The patient underwent an MRI and the imaging study demonstrated a well-defined 30 × 22 × 20-mm lesion at the anterior clinoid process with an extension to the optic canal and ethmoid sinus. The patient underwent pterional craniotomy, and the tumor was resected. The histopathological examination was suggestive of ABC.
CONCLUSIONS: ABC and other conditions should be considered in young-age people with an early unilateral decline in vision and imaging studies should be obtained in early stages and during follow-ups.
摘要:
背景:动脉瘤样骨囊肿(ABC)并不常见,良性,血管多囊性骨病变,在生命的头二十年中最常见。长骨的干phy端,骨盆,和脊柱是最常见的位置。ABCs形成的确切潜在病理生理学仍不清楚;然而,据信创伤或血管紊乱后的反应过程可能起重要作用。颅底受累很少发生,颅内ABCs的患病率高达5%。
方法:一位18岁的青春期女性,三个月前出现了进行性视力模糊的病史。脑和眼眶MRI未见异常发现。糖皮质激素治疗三个月后,诊断为多发性硬化症,左眼视力障碍突然恶化。该患者接受了MRI检查,影像学研究表明,前斜突有明确的30×22×20-mm病变,并延伸到视神经管和筛窦。病人接受了翼点开颅手术,肿瘤被切除了.组织病理学检查提示ABC。
结论:对于早期单侧视力下降的年轻人,应考虑ABC和其他情况,并应在早期和随访期间进行影像学检查。
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