PDF(Pubmed)
Abstract：
Congenital sigmoid colon stenosis is a rare entity that can mimic Hirschsprung disease. Presentation of congenital colon stenosis is usually within first few weeks of life. Our case presented with features of distal bowel obstruction at 2 years of age with the history of chronic constipation and progressive abdominal distention from first week of life and bilious vomiting for the last 1 week. Clinical diagnosis of Hirschsprung disease was made. Contrast enhanced CT abdomen showed bowel obstruction with transition point at the level of proximal sigmoid colon. There was a short segment stenosis at the level of proximal sigmoid colon. Contrast enema showed stenosis at proximal sigmoid colon. The bowel distal to stenosis was normal in calibre. Similar findings were seen during surgery. Mesocolon was present in stenosed segment of the bowel. The resected stenotic segment showed adequate ganglion cells in histopathology.
摘要：
先天性乙状结肠狭窄是一种罕见的实体，可以模仿Hirschsprung疾病。先天性结肠狭窄通常在生命的最初几周内出现。我们的病例在2岁时具有远端肠梗阻的特征，有慢性便秘和从生命的第一周开始进行性腹胀的病史，以及最后1周的胆汁性呕吐。临床诊断为先天性巨结肠。增强CT腹部显示肠梗阻，转变点位于近端乙状结肠水平。乙状结肠近端有短节段狭窄。造影剂灌肠显示乙状结肠近端狭窄。狭窄远端肠口径正常。在手术过程中也看到了类似的发现。肠系膜出现在狭窄的肠段中。切除的狭窄段在组织病理学上显示出足够的神经节细胞。
