PDF(Pubmed)
Abstract：
The authors report an unusual case of monostotic fibrous dysplasia involving the middle turbinate. Only four cases of fibrous dysplasia (FD) involving the middle turbinate had previously been documented globally, all of which entailed severe presentation and were treated surgically. We report the first case of asymptomatic monostotic FD of the middle turbinate in the Middle East, followed over a span of 10 years. Fibro-osseous lesions are rare, benign tumors of the sinonasal and orbital regions. Craniofacial FD most commonly affects the maxilla and mandible, followed by the frontal, parietal, and occipital bones. The prevalence of most patients presenting with monostotic craniofacial FD is between 10% and 29%. It is typically found incidentally, and is most likely to be asymptomatic. The risk of skull base damage and cerebrospinal fluid leaks is increased in this case due to the involvement of the middle turbinate and the expansion of FD into the lateral lamella and the cribriform plate. Our patient was managed conservatively with regular follow-up due to the minor clinical symptoms despite the extent of the disease. We aim to elucidate the specific challenges associated with middle turbinate involvement and contribute to the growing body of knowledge in this field, ultimately improving the care and quality of life for individuals affected by this condition.
摘要：
作者报告了一例涉及中鼻甲的单骨纤维结构异常。以前，全球仅有4例涉及中鼻甲的纤维发育不良（FD）病例。所有这些都需要严重的表现和手术治疗。我们报告了中东首例无症状的中鼻甲单骨FD，历时10年。纤维骨损伤很少见,鼻窦和眼眶区良性肿瘤。颅面FD最常影响上颌骨和下颌骨，紧随其后的是额叶，顶叶,和枕骨.大多数患有单骨性颅面FD的患者的患病率在10％至29％之间。它通常是偶然发现的，最有可能是无症状的。在这种情况下，由于中鼻甲的参与以及FD扩展到外侧薄片和筛板中，颅底损伤和脑脊液渗漏的风险增加。尽管疾病程度不同，但由于临床症状较小，我们的患者得到了保守的定期随访。我们的目标是阐明与中鼻甲相关的具体挑战，并有助于在这一领域不断增长的知识体系，最终改善受这种情况影响的个人的护理和生活质量。
