PDF(Pubmed)
Abstract：
BACKGROUND: As a result of the failure of embryogenic kidney formation, a condition can occur where not a single kidney appears and this phenomenon is known as unilateral renal agenesis (URA). Both aplastic and dysplastic kidney are different from renal agenesis, atrophy and renal hypoplasia. However, from this case report it can be seen that there are similarities, both radiologically and macroscopically, between cases of unilateral renal aplasia and renal agenesis.
METHODS: A 2 year old Javanese boy came to the health facility with complaints of recurrent fever and urinary tract symptoms such as dysuria and straining. Computerized Tomography (CT) scan of the abdomen and urography showed agenesis of the left kidney and a probable spina bifida. Cystourethrography examination was done and showed grade 5 voiding, then retrograde pyelography was performed with the diagnosis of unilateral renal agenesis was made because there was no visible left side collecting system even though there was a duplication in the left ureter. The next examination was carried out by histopathology and immunohistochemistry after resection of the left side of the ureter and the diagnosis increasingly pointed towards renal aplasia after primitive renal structures were found.
CONCLUSIONS: Renal agenesis and aplastic kidney are difficult to differentiate macroscopically and radiologically. Nevertheless, from this case report, we try to provide some interesting points to differentiate cases of unilateral renal agenesis from Renal Dysplasia which presents as unilateral renal aplasia.
METHODS: A 2 year old Javanese boy came to the health facility with complaints of recurrent fever and urinary tract symptoms such as dysuria and straining. Computerized Tomography (CT) scan of the abdomen and urography showed agenesis of the left kidney and a probable spina bifida. Cystourethrography examination was done and showed grade 5 voiding, then retrograde pyelography was performed with the diagnosis of unilateral renal agenesis was made because there was no visible left side collecting system even though there was a duplication in the left ureter. The next examination was carried out by histopathology and immunohistochemistry after resection of the left side of the ureter and the diagnosis increasingly pointed towards renal aplasia after primitive renal structures were found.
CONCLUSIONS: Renal agenesis and aplastic kidney are difficult to differentiate macroscopically and radiologically. Nevertheless, from this case report, we try to provide some interesting points to differentiate cases of unilateral renal agenesis from Renal Dysplasia which presents as unilateral renal aplasia.
摘要：
背景：由于胚胎性肾脏形成失败，这种情况可能发生在没有一个肾脏出现的情况下，这种现象被称为单侧肾脏发育不全（URA）。再生障碍性和发育不良的肾脏都不同于肾脏发育不全，萎缩和肾发育不全。然而,从这个病例报告可以看出有相似之处，无论是放射学还是宏观,单侧肾发育不全和肾发育不全之间的病例。
方法：一名2岁的爪哇男孩来到医疗机构，抱怨反复发烧和尿路症状，如排尿困难和紧张。腹部计算机断层扫描（CT）扫描和尿路造影显示左肾发育不全和可能的脊柱裂。做了膀胱尿道造影检查，显示5级排尿，然后进行逆行肾盂造影，诊断为单侧肾脏发育不全，因为即使左输尿管有重复，也没有可见的左侧收集系统。切除输尿管左侧后，通过组织病理学和免疫组织化学进行了下一次检查，发现原始肾结构后，诊断越来越指向肾发育不全。
结论：肾脏发育不全和再生障碍性肾难以在宏观和放射学上区分。然而，从这个病例报告中,我们试图提供一些有趣的观点，以区分单侧肾脏发育不全和表现为单侧肾脏发育不全的肾脏发育不良。
方法：一名2岁的爪哇男孩来到医疗机构，抱怨反复发烧和尿路症状，如排尿困难和紧张。腹部计算机断层扫描（CT）扫描和尿路造影显示左肾发育不全和可能的脊柱裂。做了膀胱尿道造影检查，显示5级排尿，然后进行逆行肾盂造影，诊断为单侧肾脏发育不全，因为即使左输尿管有重复，也没有可见的左侧收集系统。切除输尿管左侧后，通过组织病理学和免疫组织化学进行了下一次检查，发现原始肾结构后，诊断越来越指向肾发育不全。
结论：肾脏发育不全和再生障碍性肾难以在宏观和放射学上区分。然而，从这个病例报告中,我们试图提供一些有趣的观点，以区分单侧肾脏发育不全和表现为单侧肾脏发育不全的肾脏发育不良。
