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Abstract：
BACKGROUND: Congenital femoral deficiency (CFD) is a challenging and complex condition that causes limb lengthening. We focused on the clinical and radiographic results of SUPERhip procedures in patients with congenital femoral deficiency type 1b, according to Paley\'s classification, prior to femoral lengthening.
METHODS: We reviewed all records and radiographs of patients who underwent this procedure between 2005 and 2020. We included 26 patients, with clinical and radiographic assessments performed during pre- and post-operative evaluations.
RESULTS: There were twenty-six patients (15 right vs. 11 left), with a mean age of 7 years (1-18). Most of the patients were female (17 patients; 65.4%). Twenty (76.9%) patients were undergoing their first procedure and six (23.1%) had already undergone a previous surgery. There was a significant improvement in all radiographic parameters, with the mean preoperative and postoperative Neck-Shaft Angle (NSA) being 72.3 ± 7.1° vs. 133.1 ± 12.7°, the Center-Edge Angle (CEA) 16.8 ± 9.8° vs. 33.5 ± 14.1°, and the Acetabular Index (AI) 27.8 ± 6.9° vs. 16.4 ± 6.8°, respectively. The complication rate was 15.4%, predominantly affecting patients under 5 years old.
CONCLUSIONS: The SUPERhip procedure is an effective and reproducible technique for clinical and radiographic correction to a significant degree in patients with Paley\'s type 1b CFD, in preparation for bone lengthening surgery.
METHODS: We reviewed all records and radiographs of patients who underwent this procedure between 2005 and 2020. We included 26 patients, with clinical and radiographic assessments performed during pre- and post-operative evaluations.
RESULTS: There were twenty-six patients (15 right vs. 11 left), with a mean age of 7 years (1-18). Most of the patients were female (17 patients; 65.4%). Twenty (76.9%) patients were undergoing their first procedure and six (23.1%) had already undergone a previous surgery. There was a significant improvement in all radiographic parameters, with the mean preoperative and postoperative Neck-Shaft Angle (NSA) being 72.3 ± 7.1° vs. 133.1 ± 12.7°, the Center-Edge Angle (CEA) 16.8 ± 9.8° vs. 33.5 ± 14.1°, and the Acetabular Index (AI) 27.8 ± 6.9° vs. 16.4 ± 6.8°, respectively. The complication rate was 15.4%, predominantly affecting patients under 5 years old.
CONCLUSIONS: The SUPERhip procedure is an effective and reproducible technique for clinical and radiographic correction to a significant degree in patients with Paley\'s type 1b CFD, in preparation for bone lengthening surgery.
摘要：
背景：先天性股骨缺陷（CFD）是一种具有挑战性和复杂性的疾病，可导致肢体延长。我们专注于先天性股骨缺陷1b型患者的SUPERhip手术的临床和影像学结果，根据佩利的分类，在股骨延长之前。
方法：我们回顾了2005年至2020年间接受该手术的患者的所有记录和X光片。我们纳入了26名患者，在术前和术后评估期间进行临床和影像学评估。
结果：有26例患者（右15例与右11左），平均年龄7岁（1-18岁）。大多数患者为女性（17例；65.4％）。20例（76.9％）患者正在接受首次手术，6例（23.1％）已经接受了先前的手术。所有射线照相参数都有显著改善，术前和术后平均颈轴角（NSA）为72.3±7.1°vs.133.1±12.7°,中心边缘角度(CEA)16.8±9.8°与33.5±14.1°,和髋臼指数（AI）27.8±6.9°与16.4±6.8°,分别。并发症发生率为15.4%,主要影响5岁以下的患者。
结论：SUPERhip手术是一种有效且可重复的技术，可在Paley's1b型CFD患者中进行临床和影像学矫正，为骨延长手术做准备。
方法：我们回顾了2005年至2020年间接受该手术的患者的所有记录和X光片。我们纳入了26名患者，在术前和术后评估期间进行临床和影像学评估。
结果：有26例患者（右15例与右11左），平均年龄7岁（1-18岁）。大多数患者为女性（17例；65.4％）。20例（76.9％）患者正在接受首次手术，6例（23.1％）已经接受了先前的手术。所有射线照相参数都有显著改善，术前和术后平均颈轴角（NSA）为72.3±7.1°vs.133.1±12.7°,中心边缘角度(CEA)16.8±9.8°与33.5±14.1°,和髋臼指数（AI）27.8±6.9°与16.4±6.8°,分别。并发症发生率为15.4%,主要影响5岁以下的患者。
结论：SUPERhip手术是一种有效且可重复的技术，可在Paley's1b型CFD患者中进行临床和影像学矫正，为骨延长手术做准备。
