Abstract：
Pulmonary arterial hypertension (PAH), idiopathic pulmonary fibrosis (IPF), and scleroderma (SSc) are three interrelated medical conditions that can result in significant morbidity and mortality. Pulmonary hypertension, a condition marked by high blood pressure in the lungs, can lead to heart failure and other complications. Idiopathic pulmonary fibrosis, a progressive lung disease characterised by scarring of lung tissue, can cause breathing difficulties and impaired oxygenation. Scleroderma, an autoimmune disease, can induce thickening and hardening of the skin and internal organs, including the lungs, leading to pulmonary fibrosis and hypertension. Currently, there is no cure for any of these conditions. However, early detection and proper management can improve the quality of life and prognosis of a patient. This review focusses on PH and IPF in patients with SSc, providing information on the causes, symptoms, and treatment of these conditions, together with illustrative images. It also provides an overview of interrelated medical conditions: PH, IPF, and SSc. It emphasises the importance of early detection and proper management to improve patient quality of life and prognosis.
摘要：
肺动脉高压(PAH),特发性肺纤维化（IPF），和硬皮病（SSc）是三种相互关联的医学疾病，可导致显著的发病率和死亡率。肺动脉高压,肺部有高血压，会导致心力衰竭和其他并发症。特发性肺纤维化,一种以肺组织结疤为特征的进行性肺病，会导致呼吸困难和氧合受损。硬皮病,一种自身免疫性疾病,会引起皮肤和内脏器官的增厚和硬化，包括肺,导致肺纤维化和高血压。目前,这些情况都没有治愈方法。然而,早期发现和适当的管理可以改善患者的生活质量和预后。这篇综述集中在SSc患者的PH和IPF。提供有关原因的信息，症状,以及这些疾病的治疗，与说明性图像一起。它还提供了相关医疗条件的概述：PH，IPF,SSC。它强调了早期发现和适当管理以改善患者生活质量和预后的重要性。
