PDF(Pubmed)
Abstract：
Microspherophakia constitutes a rare, mostly bilateral anomaly of the crystalline lens, which is characterized by the presence of an increased lens thickness and reduced equatorial diameter. It is frequently associated with lens subluxation, translating into a high degree of variable lenticular myopia and defective accommodation. The purpose of this report is to describe the treatment of a three-year-old female patient with microspherophakia, with the scleral fixation of an intraocular lens using the z-suture technique. A three-year-old female patient with Marfan Syndrome presented with high bilateral myopia and esotropia. Lens subluxation was perceived, and she was proposed for bilateral surgery. Scleral fixation of the intraocular lens was performed using the z-suture technique. During the five-year follow-up period, she maintained a best-corrected visual acuity of 20/20 in both eyes wearing bifocal glasses. Microspherophakia is a rare but impactful condition, frequently related to severe and variable refractive error due to the lens shape and zonule instability. Intraocular lens implantation in the capsular bag is usually impossible, and scleral fixation is a valid alternative. The z-suture technique avoids suture knots and the need for intrascleral flaps, reducing the risk of suture-related complications.
摘要：
微球构成一种罕见的，主要是双侧晶状体异常，其特征在于存在增加的透镜厚度和减小的赤道直径。它经常与晶状体脱位有关，转化为高度可变的双凸透镜近视和有缺陷的调节。本报告的目的是描述一名三岁女性患者的治疗方法，使用z缝合技术对人工晶状体进行巩膜固定。3岁女性马凡氏综合征患者表现为双侧高度近视和内斜视。感觉到晶状体半脱位，她被提议进行双侧手术。使用z缝合技术进行人工晶状体的巩膜固定。在五年的后续行动期间，她戴双焦点眼镜的双眼保持20/20的最佳矫正视力。微球是一种罕见但有影响的疾病，由于晶状体形状和小带不稳定，通常与严重和可变的屈光不正有关。在囊袋内植入人工晶状体通常是不可能的，巩膜固定术是一种有效的替代方法。z缝合技术避免了缝合结和巩膜内皮瓣的需要，降低缝合相关并发症的风险。
