Abstract：
Urethral atresia is a rare but clinically significant cause of congenital lower urinary tract obstruction. Initial management options include urinary diversion until definitive urethral reconstruction or progressive urethral dilation. Given the overall rarity of the condition, there are no evidence-based guidelines for the immediate and long-term management of urethral atresia, and clinical practice varies widely. We present an illustrative case managed with progressive urethral dilation alongside urinary diversion to highlight key factors in shared clinical decision making. Ultimately, pooled multi-institutional long-term outcomes data are needed to better guide practice for these patients and their families.
摘要：
尿道闭锁是先天性下尿路梗阻的罕见但具有临床意义的原因。最初的治疗选择包括尿流改道，直到确定的尿道重建或进行性尿道扩张。鉴于这种情况的总体罕见性，对于尿道闭锁的即时和长期治疗,目前尚无循证指南,而且临床实践差异很大.我们提出了一个说明性的案例，该案例通过进行性尿道扩张和尿流改道进行管理，以强调共同临床决策中的关键因素。最终,需要汇集多机构长期结局数据,以更好地指导这些患者及其家属的实践.
