关键词: Cogan's syndrome Deafness Surdité Syndrome de Cogan Uveitis Uvéite Vascularite Vasculitis

Mesh : Female Humans Adult Cogan Syndrome / complications diagnosis Keratitis / diagnosis Cochlear Implants Syndrome Autoimmune Diseases Apraxias / congenital

来  源:   DOI:10.1016/j.jfo.2023.104044

Abstract:
Cogan\'s syndrome is a rare autoimmune inflammatory disease, characterized by interstitial keratitis and audio-vestibular signs. The syndrome was first described in 1945 by David G. Cogan. Then, it was only in 1980 when Haynes et al. proposed diagnostic criteria for patients with other symptoms and was qualified as atypical form of Cogan\'s syndrome. Herein, we report a case of a 28-year-old woman with atypical Cogan\'s syndrome. The patient was treated with corticosteroids and received a cochlear implant.
摘要:
Cogan综合征是一种罕见的自身免疫性炎症性疾病,以间质性角膜炎和音频前庭体征为特征。该综合征于1945年由DavidG.Cogan首次描述。然后,直到1980年Haynes等人.提出了有其他症状的患者的诊断标准,并被认为是Cogan综合征的非典型形式。在这里,我们报告一例28岁女性非典型Cogan综合征。患者接受皮质类固醇治疗,并接受人工耳蜗植入。
公众号