PDF(Pubmed)
Abstract：
Amelogenesis imperfecta is a rare genetic disorder that interferes with normal enamel formation. Of the 4 main types of amelogenesis imperfecta, hypoplastic (type 1) is the most prevalent, characterized by a quantitative alteration in enamel. The pitting or reduced thickness of the enamel results in generalized hypersensitivity, increased susceptibility to caries and infection, attrition, and a loss in vertical dimension of occlusion. Prosthodontic management of these patients can be challenging not only functionally and restoratively, but also from an emotional and psychosocial standpoint. This clinical report describes the prosthodontic management and rehabilitation of two young adult siblings with hypoplastic (type 1) amelogenesis imperfecta.
摘要：
成釉细胞不全症是一种罕见的遗传性疾病，会干扰正常的牙釉质形成。在釉质发育不全症的4种主要类型中，发育不良(1型)是最普遍的，以牙釉质的定量变化为特征。牙釉质的点蚀或厚度减少会导致全身过敏，对龋齿和感染的易感性增加，自然减员,以及遮挡垂直维度的损失。这些患者的修复治疗不仅在功能上和修复上都具有挑战性，而且从情感和社会心理的角度来看。本临床报告描述了两名患有发育不良（1型）牙釉质发育不全的年轻成年兄弟姐妹的修复治疗和康复。
