Abstract:
A 17-year-old boy with typical neurodevelopment presented with 3 months of lower-limb weakness without a history of trauma. Physical examination, plain radiography and a T2-weighted MRI revealed a port-wine stain over the lumbar region, significant scoliosis below the cervical segment, and a multifocal flow void sign (steal phenomenon) from epidural space to dorso-lumbar spine, respectively (Figure 1). CT angiography identified an enhancing dorsal vascular mass with involvement of the spinal canal including destruction of the vertebral body determined to be extensive arteriovenous shunts on digital subtraction angiography (DSA) (Figure 2).
摘要:
一个17岁的男孩,具有典型的神经发育,表现为下肢无力3个月,没有外伤史。体格检查,X线平片和T2加权MRI显示腰椎区域有葡萄酒色斑,颈段以下显著脊柱侧凸,以及从硬膜外腔到背腰椎的多灶性血流空征(偷窃现象),分别(图1)。CT血管造影确定增加的背侧血管肿块,累及椎管,包括椎体的破坏,在数字减影血管造影(DSA)上确定为广泛的动静脉分流(图2)。