Abstract：
Hypomyelination of early myelinating structures (HEMS) has recently been defined as a new genetic disorder accompanied by clinical and MR imaging characteristics. However, no studies have focused on diffusion-weighted imaging (DWI) findings of HEMS. We would like to propose a \"sheep sign,\" which is formed by DWI hyperintensity in the medial medullary lamina along with alternating high-low-high (HLH) intensity stripes in the posterior limb of the internal capsule. We believe the presence of the \"sheep sign\" on DWI in combination with alternating HLH intensity stripes may be a valuable tool for diagnosing HEMS.
摘要：
最近，早期髓鞘结构（HEMS）的髓鞘减少被定义为一种新的遗传性疾病，伴有临床和MR影像学特征。然而,没有研究关注HEMS的弥散加权成像(DWI)结果.我们想提出一个\"羊的标志，“由内侧延髓层的DWI高强度以及内囊后肢的高低高（HLH）强度条纹交替形成。我们相信DWI上“绵羊标志”的存在与交替的HLH强度条纹相结合可能是诊断HEMS的有价值的工具。
