External Esophageal Stenting Technique in Palliation for Tracheal Agenesis in a Case of Esophageal Lung: A Lesson Learned from the Experience for Tracheomalacia.

食管外支架置入技术在一例食管肺气管道发育不全姑息中的应用 ： 从气管软化的经验中汲取的教训。

• 影响指数: 2.835
• 发表时间: 2023 Dec 10
• 来源期刊: Children (Basel)
• DOI: 10.3390/children10121907
• PMID: 38136109
• 文章类型: Case Reports
• 作者列表: Hirotani T,Tamura R,Ando M,Okajima H

关键词: dying spell; esophageal lung; external stenting; tracheal agenesis; tracheomalacia

Abstract

Tracheal agenesis (TA) is a rare congenital anomaly with an incidence of 1 per 50,000 newborns. It appears at birth with severe respiratory distress, cyanosis, and inaudible crying. Prompt esophageal intubation and long-term management of the esophageal airway are essential to overcome this catastrophic condition. In the long-term management, external stenting of the esophageal airway has been reported as promising to support the fragile esophageal wall; this technique was taken from the surgery for tracheomalacia. We experienced a case of an infant with tracheal agenesis whose respiratory status was stabilized after external esophageal stenting. The stenting was performed based on a lesson learned in the extensive experience in the surgical treatment for tracheomalacia, and the surgical techniques for successful stenting are herein described.

摘要

气管发育不全（TA）是一种罕见的先天性异常，每50,000例新生儿中就有1例。它在出生时出现严重的呼吸窘迫，紫癜,听不见的哭声。及时的食管插管和食管气道的长期管理对于克服这种灾难性状况至关重要。在长期管理中,据报道，食管气道外支架有望支持脆弱的食管壁；这项技术取自气管软化症的手术。我们经历了一例气管发育不全的婴儿，其在外部食管支架置入后呼吸状态稳定。支架置入术是根据在气管软化手术治疗中的丰富经验而获得的。本文描述了用于成功置入支架的手术技术。