PDF(Pubmed)
Abstract：
Malignant peripheral nerve sheath tumors are soft tissue sarcomas originating from peripheral nerves. They are more frequently diagnosed in individuals with neurofibromatosis and tend to affect young men more often than women. The most common sites for these tumors within the peripheral nerve sheath are in the pelvis and the distal femur. Although chemotherapy and radiotherapy are not frequently used, it should be noted that in some cases, postoperative radiotherapy and chemotherapy may be beneficial. The primary treatment approach typically involves the complete surgical removal of the tumor. Here, we discuss the case of our patient whom we successfully treated with extensive resection and followed up with postoperative radiotherapy at our clinic.
摘要：
恶性周围神经鞘瘤是起源于周围神经的软组织肉瘤。它们在患有神经纤维瘤病的个体中更频繁地被诊断,并且倾向于比女性更频繁地影响年轻男性。这些肿瘤在外周神经鞘中最常见的部位是骨盆和股骨远端。虽然化疗和放疗并不经常使用，应该指出的是，在某些情况下，术后放疗和化疗可能是有益的。主要治疗方法通常涉及完全手术切除肿瘤。这里,我们讨论了我们的病人的情况下，我们成功地进行了广泛的切除和随访术后放疗在我们的诊所。
