Abstract：
Primary sebaceous carcinoma of the lacrimal gland (PSCLG) is the rarest lacrimal gland (LG) tumor, often belatedly diagnosed, worsening the prognosis. We present a 68-year-old man with a large, indurated mass in the left orbital outer quadrant, visible at the conjunctival upper temporal fornix, extending to the lower fornix, with left gaze restriction. The lesion was not related to the eyelid or other periocular tissues. Excisional biopsy revealed the PSCLG diagnosis. There are only eight others previous PSCLGs. Males are the most affected. Indurated mass in the lacrimal fossa, with eyelid in \"S\" shape is the most common presentation. Image exams are suggestive, but histological and immunohistochemical evaluations showing a single tumor cell line within LG are mandatory for definitive diagnosis. Larger and more extensive lesions can have a poor prognosis, but early detection can favor the outcome.
摘要：
原发性泪腺皮脂腺癌（PSCLG）是最罕见的泪腺（LG）肿瘤，经常迟来的诊断，恶化预后。我们给一个68岁的男人一个大的,左眼眶外象限的肿块,在结膜颞上穹窿处可见，延伸到下穹窿，左凝视限制。病变与眼睑或其他眼周组织无关。切除活检显示PSCLG诊断。以前的PSCLG只有八个。男性受影响最大。泪囊窝的饱和肿块，眼睑呈“S”形是最常见的表现。图像检查很有启发性，但是组织学和免疫组织化学评估显示LG中的单个肿瘤细胞系对于明确诊断是强制性的。较大和更广泛的病变可能预后不良，但是早期发现可以有利于结果。
