Abstract：
The patient was a 27-year-old man. He was referred to our hospital because he was aware of a mass in his abdomen. An abdominal ultrasound showed a 70-mm mass lesion. Enhanced computed tomography showed a 70-mm mass with well- defined margins and heterogeneous internal enhancement near the proximal jejunum. The patient was diagnosed with a suspected primary submucosal tumor of the duodenum or small intestine, and surgery was planned to diagnose and treat the tumor. The tumor was located in the upper jejunal mesentery, and tumor resection and partial small bowel resection were performed. Histopathological examination revealed proliferation of spindle-shaped cells without karyomitosis, and mixed collagen fibers in the tissue. Immunohistochemistry showed β-catenin(+), SMA(+), AE1/AE3(-), KIT(-), CD34(-), and S-100(-). Based on these findings, we diagnosed primary desmoid fibromatosis of the small intestinal mesentery. In this report, we describe a case of primary desmoid fibromatosis of the small intestinal mesentery with a review of the literature.
摘要：
病人是一名27岁的男子。他被转诊到我们医院，因为他知道腹部有肿块。腹部超声显示70毫米的肿块病变。增强的计算机断层扫描显示70毫米的肿块，边缘清晰，近端空肠附近的内部增强不均匀。患者被诊断为十二指肠或小肠原发性粘膜下肿瘤，并计划手术来诊断和治疗肿瘤。肿瘤位于空肠上肠系膜,肿瘤切除和部分小肠切除。组织病理学检查显示梭形细胞增殖，无核分裂，和组织中混合的胶原纤维。免疫组织化学显示β-catenin(+),SMA(+),AE1/AE3(-),KIT(-),CD34(-),S-100（-）。基于这些发现,我们诊断为原发性小肠系膜纤维瘤病。在这份报告中,我们描述了一例原发性小肠系膜纤维瘤病，并回顾了文献。
