关键词: membranous supravalvular aortic stenosis ultrasonography

Mesh : Humans Aortic Stenosis, Supravalvular / complications diagnostic imaging surgery Aortic Valve Insufficiency / complications diagnostic imaging surgery Aortic Valve Stenosis

来  源:   DOI:10.1002/jcu.23621

Abstract:
Although the clinical manifestations of membranous supravalvular aortic stenosis (SVAS) are distinctive, its diagnosis remains challenging. Failure to initiate surgical treatment in a timely manner greatly increases the risk of sudden cardiac death. We report a case of membranous SVAS, detailing the clinical presentation and imaging manifestations.
摘要:
尽管膜瓣上主动脉瓣狭窄(SVAS)的临床表现是独特的,它的诊断仍然具有挑战性。未能及时开始手术治疗会大大增加心源性猝死的风险。我们报告一例膜性SVAS,详细介绍临床表现和影像学表现。
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