PDF(Pubmed)
Abstract：
Since the first description of apical hypertrophic cardiomyopathy (ApHCM) in 1976, contrasting information from all over the world has emerged regarding the natural history of the disease. However, the recommended guidelines on hypertrophic cardiomyopathy (HCM) pay a cursory reference to ApHCM, without ApHCM-specific recommendations to guide the diagnosis and management. In addition, cardiologists may not be aware of certain aspects that are specific to this disease subtype, and a robust understanding of specific disease features can facilitate recognition and timely diagnosis. Therefore, the review covers the incidence, pathogenesis, and characteristics of ApHCM and imaging methods. Echocardiography and cardiovascular magnetic resonance imaging (CMR) are the most commonly used imaging methods. Moreover, this review presents the management strategies of this heterogeneous clinical entity. In this review, we introduce a novel transapical beating-heart septal myectomy procedure for ApHCM patients with a promising short-time result.
摘要：
自1976年首次描述心尖肥厚型心肌病（ApHCM）以来，来自世界各地的有关该疾病自然史的对比信息已经出现。然而,关于肥厚型心肌病（HCM）的推荐指南粗略地参考了ApHCM，没有针对ApHCM的特定建议来指导诊断和管理。此外,心脏病学家可能不知道这种疾病亚型特有的某些方面，对特定疾病特征的强大了解可以促进识别和及时诊断。因此,审查涵盖了发病率，发病机制，ApHCM的特点和成像方法。超声心动图和心血管磁共振成像（CMR）是最常用的成像方法。此外，这篇综述介绍了这种异质性临床实体的管理策略.在这次审查中,我们为ApHCM患者介绍了一种新颖的经心尖搏动-心间隔肌切除术，具有良好的短期效果。
