Abstract：
A 27-year-old female patient presented with chronic spontaneous cerebrospinal fluid (CSF) rhinorrhea. She had deformity and weakness on the left side since childhood. Imaging examinations demonstrated hemi-hydranencephaly with a nearly complete absence of the right cerebral hemisphere, which was replaced with a membranous sac filled with CSF. She was accompanied with a frontal midline tumor containing lipids. After ventriculoperitoneal shunt, the CSF rhinorrhea completely ceased and no direct repair of the CSF fistula was necessary. The ventriculoperitoneal shunt procedure changes the CSF flow dynamics and releases the intracranial pressure, which may be a simple and effective procedure for CSF rhinorrhea in hemi-hydranencephaly.
摘要：
一名27岁的女性患者出现慢性自发性脑脊液（CSF）鼻漏。她从小就有左侧的畸形和虚弱。影像学检查显示，右脑半球几乎完全缺失，用充满CSF的膜囊代替。她伴有含脂质的额叶中线肿瘤。脑室-腹腔分流术后,脑脊液鼻漏完全停止,无需直接修复脑脊液瘘.脑室-腹腔分流术改变脑脊液血流动力学并释放颅内压,这可能是一种简单有效的方法，用于治疗半水无脑症的脑脊液鼻漏。
