PDF(Pubmed)
Abstract：
Fibrous dysplasia (FD) is a rare skeletal disorder characterized by abnormal fibro-osseous connective tissue replacing normal bone. Despite its benign behavior, craniofacial FD can cause morphological disfigurement, headache, and even blindness as a result of the produced mass effect. Surgical resection is recommended when the patient shows apparent clinical symptoms or aggravating facial asymmetry. Postoperative complications have been reported, such as hematoma, surgical site infection, abscess formation, resorption of the bone graft used for reconstruction, and recurrence. An aneurysmal bone cyst (ABC) is a rare benign bony lesion that can occur secondary to preexisting bone tumor. Secondary ABCs in craniofacial FD are extremely rare in the literature, accounting for less than 30, all of which are either case reports or series. We report an extremely rare case of symptomatic secondary ABC arising from craniofacial FD that had been misdiagnosed with abscess formation or recurrence and was surgically removed. Notably, 17 years elapsed between the primary surgery and the complication of secondary ABC. The patient underwent total removal of secondary ABC. After surgery, symptoms were relieved, with no recurrence observed during a 6-month follow-up.
摘要：
纤维发育不良（FD）是一种罕见的骨骼疾病，其特征是异常的纤维骨结缔组织替代正常骨。尽管它的行为是良性的，颅面FD会导致形态学毁容，头痛,甚至由于产生的大规模效应而失明。当患者出现明显的临床症状或加重面部不对称时，建议手术切除。术后并发症已有报道，如血肿，手术部位感染,脓肿形成,用于重建的骨移植物的吸收，和复发。动脉瘤性骨囊肿（ABC）是一种罕见的良性骨性病变，可继发于先前存在的骨肿瘤。颅面FD中的继发性ABCs在文献中极为罕见，占30以下，全部为病例报告或系列。我们报告了因颅面FD引起的有症状的继发性ABC的极为罕见的病例，该病例被误诊为脓肿形成或复发，并通过手术切除。值得注意的是,从初次手术到二次ABC的并发症之间经过了17年。患者接受了二次ABC的完全切除。手术后,症状缓解,在6个月的随访中没有观察到复发。
