METHODS: We report a 32-year-old male patient with multi-segmental spinal Rosai-Dorfman disease. On admission, his left fingers had been numb for 2 months. Over a 2-month period, the limb numbness progressed from the left to the right hand. The patient underwent resection of the lesion and internal fixation of the C2-C7 spine. The postoperative outcomes were satisfied and no recurrence was observed at 1-year follow-up.
CONCLUSIONS: Spinal Rosai-Dorfman disease is a relatively rare tumor of which the pathogenesis is still unclear, and most patients have no specific clinical manifestations. Characteristic imaging findings can indicate this disease, however, a definitive diagnosis still depends on a pathological examination. Currently, total surgical resection of the tumor is a relatively effective and preferred treatment.
方法:我们报告了一名32岁男性多节段脊柱Rosai-Dorfman病患者。一入场,他的左手手指已经麻木了两个月。在两个月的时间里,肢体麻木从左手发展到右手。患者接受了C2-C7脊柱的病变切除和内固定。术后疗效满意,随访1年无复发。
结论:脊柱Rosai-Dorfman病是一种相对罕见的肿瘤,其发病机制尚不清楚。大多数患者没有特异性的临床表现。特征性影像学表现可以提示这种疾病,然而,明确的诊断仍然取决于病理检查。目前,手术切除肿瘤是一种相对有效的首选治疗方法。