PDF(Pubmed)
Abstract：
UNASSIGNED: Congenital pulmonary hypoplasia (CPH) is a rare pulmonary disease featured by incomplete development of pulmonary tissues. Its diagnosis is still a challenge as patients are usually misdiagnosed as atelectasis.
UNASSIGNED: A female neonate was admitted to our hospital due to post-birth jaundice for 12 hrs. Physical examination showed accelerated breathing. There was no respiratory sound in the left lung. Chest film indicated decline of lucency in the left lung. Chest CT scan indicated absence of left lung and primary bronchus of the left lung. The boundary between left mediastinum was not clearly displayed. Three-dimensional CT scan indicated absence of left lung and left principal bronchus. Cardiac ultrasonography confirmed congenital heart disease. She showed ectopic kidney. Finally, she was diagnosed with CPH concurrent with congenital heart disease and ectopic kidney.
UNASSIGNED: On 17-month follow-up visit, the patient is still survived, but she presents with obstruction in ventilation function.
UNASSIGNED: A female neonate was admitted to our hospital due to post-birth jaundice for 12 hrs. Physical examination showed accelerated breathing. There was no respiratory sound in the left lung. Chest film indicated decline of lucency in the left lung. Chest CT scan indicated absence of left lung and primary bronchus of the left lung. The boundary between left mediastinum was not clearly displayed. Three-dimensional CT scan indicated absence of left lung and left principal bronchus. Cardiac ultrasonography confirmed congenital heart disease. She showed ectopic kidney. Finally, she was diagnosed with CPH concurrent with congenital heart disease and ectopic kidney.
UNASSIGNED: On 17-month follow-up visit, the patient is still survived, but she presents with obstruction in ventilation function.
摘要：
■先天性肺发育不全（CPH）是一种罕见的肺部疾病，其特征是肺组织发育不完全。由于患者通常被误诊为肺不张，因此其诊断仍然是一个挑战。
一名女性新生儿因出生后黄疸12小时入院。体格检查显示呼吸加快。左肺无呼吸音。胸膜提示左肺透明度下降。胸部CT示：左肺及左肺原发性支气管缺失。左纵隔之间的边界未清楚显示。三维CT示：左肺、左主支气管缺如。心脏超声检查证实先天性心脏病。她表现为肾脏异位。最后,她被诊断为CPH并发先天性心脏病和异位肾。
■在17个月的随访中，病人仍然存活，但她表现出通气功能受阻。
一名女性新生儿因出生后黄疸12小时入院。体格检查显示呼吸加快。左肺无呼吸音。胸膜提示左肺透明度下降。胸部CT示：左肺及左肺原发性支气管缺失。左纵隔之间的边界未清楚显示。三维CT示：左肺、左主支气管缺如。心脏超声检查证实先天性心脏病。她表现为肾脏异位。最后,她被诊断为CPH并发先天性心脏病和异位肾。
■在17个月的随访中，病人仍然存活，但她表现出通气功能受阻。
