PDF(Pubmed)
Abstract：
Ascending aortic aneurysm is very rare in children, and is usually seen in patients with underlying connective tissue disorders such as Marfans and Ehler-Danlos syndrome. Loeys-Dietz syndrome (LDS) is less commonly seen as a cause of ascending aortic aneurysms in children. In this case report, we describe pediatric Bentall procedure, which we successfully performed to a child with LDS (Type I) with giant ascending aortic enlargement and significant aortic regurgitation.
摘要：
升主动脉瘤在儿童中非常罕见，通常见于患有潜在结缔组织疾病的患者，例如Marfans和Ehler-Danlos综合征。Loeys-Dietz综合征（LDS）很少被视为儿童升主动脉瘤的病因。在这个案例报告中,我们描述了小儿Bentall手术，我们成功地对患有LDS（I型）的儿童进行了治疗，这些儿童患有巨大的升主动脉扩大和显着的主动脉瓣反流。
