关键词: afferent pupillary defect atypical findings diabetes insipidus elevated intraocular pressure headache disorders neuro-endocrine disorder rathke's pouch recurrent craniopharyngioma suprasellar tumor visual field loss

来  源:   DOI:10.7759/cureus.45493   PDF(Pubmed)

Abstract:
Craniopharyngiomas are benign epithelial tumors derived from the suprasellar region of the brain. The classical presentation of midline craniopharyngiomas includes bitemporal hemianopsia. However, atypical presentations can lead to diagnosis delays and challenges in managing associated visual and endocrine deficits. The persistence of visual deficits and tumor regrowth despite surgical intervention emphasizes the intricacies of craniopharyngioma management. This underscores the significance of timely diagnosis in patients with visual disturbances and hormonal imbalances related to mass effect. Here, we present a case of a unique and rare recurrent craniopharyngioma in a 58-year-old male, featuring progressive and atypical visual disturbances, along with the development of endocrine dysfunction following multiple tumor resections.
摘要:
颅咽管瘤是源自脑鞍上区域的良性上皮肿瘤。中线颅咽管瘤的经典表现包括双颞侧偏盲。然而,非典型表现可能导致诊断延迟和管理相关视觉和内分泌缺陷方面的挑战.尽管进行了手术干预,但视力缺陷和肿瘤再生的持续存在强调了颅咽管瘤治疗的复杂性。这强调了及时诊断视觉障碍和与质量效应相关的激素失衡的患者的重要性。这里,我们介绍了一个58岁男性的独特和罕见的复发性颅咽管瘤,以渐进性和非典型视觉障碍为特征,随着多发性肿瘤切除后内分泌功能障碍的发展。
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